KMID : 0882420160900020132
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Korean Journal of Medicine 2016 Volume.90 No. 2 p.132 ~ p.135
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Paroxysmal Nocturnal Hemoglobinuria Presenting as Recurrent Jejunitis
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±èÁö¿ø:Kim Ji-Won
±èÁØ¿µ:Kim Jun-Young/±èÁøÇý:Kim Jin-Hae/±èÇýÀÎ:Kim Hye-In/±è¿µ³²:Kim Young-Nam/±è¿µÈ£:Kim Young-Ho/È«¼º³ë:Hong Sung-Noh
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Abstract
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Paroxysmal nocturnal hemoglobinuria (PNH) is a rare acquired hematopoietic stem cell disorder characterized by chronic complement-mediated intravascular hemolysis, nocturnal hemoglobinuria, predisposition to thrombosis and secondary bone marrow failure. Small bowel ischemia is a complication of PNH but has not been reported to date in a Korean adult. We report here a case of PNH presenting as recurrent jejunitis. Despite the uncommon etiology, PNH should be considered in the differential diagnosis of patients with unexplained recurrent jejunitis.
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KEYWORD
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Jejunitis, Paroxysmal nocturnal hemoglobinuria, Thrombosis, Small bowel ischemia
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