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KMID : 0882420160900020132
Korean Journal of Medicine
2016 Volume.90 No. 2 p.132 ~ p.135
Paroxysmal Nocturnal Hemoglobinuria Presenting as Recurrent Jejunitis
±èÁö¿ø:Kim Ji-Won
±èÁØ¿µ:Kim Jun-Young/±èÁøÇý:Kim Jin-Hae/±èÇýÀÎ:Kim Hye-In/±è¿µ³²:Kim Young-Nam/±è¿µÈ£:Kim Young-Ho/È«¼º³ë:Hong Sung-Noh
Abstract
Paroxysmal nocturnal hemoglobinuria (PNH) is a rare acquired hematopoietic stem cell disorder characterized by chronic complement-mediated intravascular hemolysis, nocturnal hemoglobinuria, predisposition to thrombosis and secondary bone marrow failure. Small bowel ischemia is a complication of PNH but has not been reported to date in a Korean adult. We report here a case of PNH presenting as recurrent jejunitis. Despite the uncommon etiology, PNH should be considered in the differential diagnosis of patients with unexplained recurrent jejunitis.
KEYWORD
Jejunitis, Paroxysmal nocturnal hemoglobinuria, Thrombosis, Small bowel ischemia
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